以黄疸为特征的原发性肝淀粉样变性1例报告

鲍旭丽; 田洲; 陈庆峰; 李丽; 张蕾; 闾军

doi:10.3969/j.issn.1001-5256.2013.12.018

以黄疸为特征的原发性肝淀粉样变性1例报告

DOI: 10.3969/j.issn.1001-5256.2013.12.018

1. 首都医科大学附属北京佑安医院肝病与肿瘤生物治疗科
2. 安徽省宿州市立医院感染科

基金项目:

北京市卫生系统高层次卫生技术人才培养项目资助(2011-J.L.)；首都医学发展科研基金(2009-3156)；

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中图分类号: R575.5
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出版历程
- 出版日期: 2013-12-20

One case of primary hepatic amyloidosis characterized by jaundice

Department of Hepatopathy and Cancer Biotherapy, Beijing Youan Hospital, Capital Medi cal University

Research funding:

摘要

摘要: <正>淀粉样变性是由不溶性淀粉样蛋白沉积在组织器官中引起的一类进行性、预后不良的疾病,主要可分为原发性(淀粉样物质为免疫球蛋白的轻链,AL型)和继发性(淀粉样物质为淀粉A蛋白,AA型)。AL型常累及肝、肾、脾、心脏、胃肠及皮肤等多个组织器官[1],以往的尸解发现95%的原发性淀粉样变性患者都有肝脏淀粉样物质沉积[2]。AA型常继发于多发性骨髓瘤、
- 淀粉样变性 /
- 肝疾病 /
- 黄疸
- amyloidosis /
- liver disease /
- jaundice

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参考文献(12)

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