胰腺错构瘤1例报告

摘要: 胰腺错构瘤是一种罕见的胰腺良性病变，缺乏典型的临床症状和影像学特征，术前难以诊断。常由于无法排除恶性肿瘤的风险而行外科手术治疗，从而造成正常胰腺组织的损伤。此外，胰腺错构瘤中出现胃黏膜组织尚未有报道，本文同时回顾了国内外有关胰腺错构瘤的文献，总结其临床表现及影像学特点，有助于术前诊断。
- 胰腺肿瘤 /
- 错构瘤 /
- 诊断，鉴别
Abstract: Pancreatic hamartoma is a rare benign lesion of the pancreas characterized by a lack of typical clinical symptoms and imaging features， which leads to the difficulty in diagnosis before surgery. Since surgical intervention is often performed due to the inability to exclude the risk of malignant tumor， it may cause damage to normal pancreatic tissue. In addition， the presence of gastric mucosal tissue in pancreatic hamartoma has not been reported in the literature. This article reviews the articles on pancreatic hamartoma in China and globally and summarizes its clinical and imaging features， so as to provide help for preoperative diagnosis.
- Pancreatic Neoplasms /
- Hamartoma /
- Diagnosis， Differential

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图 1 胰腺错构瘤患者腹部增强CT

注： a，平扫示胰腺颈部肿块，囊实性成分，低密度（箭头所示）；b、c，实性成分在动脉期和静脉期不均匀渐进性强化。

Figure 1. Abdominal contrast-enhanced computed tomography findings of the patient with pancreatic hamartoma

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图 2 胰腺错构瘤患者的病理结果（HE染色，×100）

注： a，病变主要由胃壁黏膜组织组成，周围环绕固有肌层组织；b，镜下见密集的柱状上皮细胞，周边结缔组织，无恶性或不典型增生细胞的迹象。

Figure 2. Pathological findings of the patient with Pancreatic hamartoma （HE staining， ×100）

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