原发性肝淀粉样变性1例报告

李晨; 陈婧; 刘鸿凌; 朱冰; 臧红; 游绍莉; 辛绍杰

doi:10.3969/j.issn.1001-5256.2013.10.017

原发性肝淀粉样变性1例报告

DOI: 10.3969/j.issn.1001-5256.2013.10.017

解放军第302医院肝衰竭诊疗与研究中心

基金项目:

“十二五”国家传染病科技重大专项(2012ZX10002004-005)；

详细信息

中图分类号: R575.5
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出版历程
- 出版日期: 2013-10-20

One case of primary hepatic amyloidosis

Liver Failure Treatment and Research Centre, 302 Hospital of PLA

Research funding:

摘要

摘要: <正>淀粉样变性,又称淀粉样物质沉积症,是以淀粉样物质在各种组织和脏器细胞外间隙沉积为特征的一种进行性疾病,主要累及心、肝、肾、脾、胃肠、肌肉、皮肤、神经系统等部位,当发生于肝脏时,则称为肝淀粉样变性[1]。根据淀粉样物质中纤维蛋白前体的化学结构种类,淀粉样变性分为6种临床类型,即原发性淀粉样变性、继发性淀粉样变性、透析相关性淀粉样变性、家族性淀粉样变性、老年性淀粉样变性、局限性淀粉样变性[2]。该病整体发病率低,其中原发性淀粉样变
- 肝疾病 /
- 淀粉样变性
- liver diseases /
- amyloidosis

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参考文献(14)

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