Portal hypertension as the main clinical manifestations of myelofibrosis with acute cholecystitis: a case report
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摘要: <正>1病例资料患者女性,42岁,因"间断腹胀8年,便血1 d"入院。患者于8年前出现乏力、腹胀,行相关检查后诊断为"门静脉高压症、门静脉血栓、脾静脉血栓及肠系膜上静脉血栓"。后患者反复出现腹腔积液、胸腔积液、间断利尿治疗;1个月前患者出现气短,活动后加重。1 d前出现便血,量约1000 ml,暗红色,同时伴有心慌、大汗、一过性意识丧失,为治疗急诊入院。查
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Key words:
- hypertension /
- portal /
- myelofibrosis /
- cholecystitis
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[1]ZHANG DY,SHI H,ZHANG SC,et al.Portal hypertension secondary to primary myelofibrosis:a case report and review of literatures[J].Chin J Clin Med,2013,20(2):230-232.(in Chinese)张丹瑛,石虹,张顺财,等.原发性骨髓纤维化合并门脉高压症1例报告并文献复习[J].中国临床医学,2013,20(2):230-232. [2]YAN M,ZHANG MH.A retrospective analysis of myelofibrosis with portal hypertension as a major manifestation[J].Chin J Hematol,1998,19(10):551.(in Chinese)阎明,张茂宏.以门静脉高压为主要表现的骨髓纤维化回顾分析[J].中华血液学杂志,1998,19(10):551. [3]MUGHAL TI,VADDI K,SARLIS NJ,et al.Myelofibrosis-associated complications:pathogenesis,clinical manifestations,and effects on outcomes[J].Int J Gen Med,2014,7:89-101.
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