累及肝内胆管的先天性胆管扩张症:外科治疗的进展、难点与争议

杨世忠; 项灿宏

doi:10.3969/j.issn.1001-5256.2017.02.011

累及肝内胆管的先天性胆管扩张症:外科治疗的进展、难点与争议

DOI: 10.3969/j.issn.1001-5256.2017.02.011

清华大学附属北京清华长庚医院肝胆外科

详细信息

中图分类号: R657.44
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- 被引次数: 0
出版历程
- 收稿日期: 2016-11-29
- 出版日期: 2017-02-20

Surgical treatment of congenital bile duct dilatation with involvement of the intrahepatic bile duct:advances,difficulties,and controversy

Department of Hepatobiliary Surgery,Beijing Tsinghua Changgund Hospital,Tsinghua University

摘要

摘要: 先天性胆管扩张症可发生在胆道树的任何部位,其中累及肝内胆管的病变在诊治方面最具挑战性。外科手术在先天性胆管扩张症的治疗中占据主导地位,手术目的在于缓解症状、防止病情进展和恶性转化。手术的原则是彻底去除病灶,建立通畅的胆汁引流通道。针对肝内胆管受累的先天性胆管扩张症,手术方式主要是肝切除,弥漫性病变可采取肝移植。因此,采取积极肝切除和早期干预的策略将使患者获益最大。
- 胆管疾病 /
- 胆总管囊肿 /
- 肝切除术 /
- 诊断
Abstract: Congenital bile duct dilatation may occur in any part of the biliary tree,and the diagnosis and treatment of lesions involving the intrahepatic bile duct is the most challenging issue.Surgical operation plays a dominant role in the management of congenital bile duct dilatation,with the purposes of relieving symptoms and preventing disease progression and malignant transformation.Surgical principles are radical resection of lesions and reconstruction of unobstructed bile drainage.Hepatectomy is the main surgical procedure for congenital bile duct dilatation with involvement of the intrahepatic bile duct,and liver transplantation can be used for diffuse lesions.Therefore,we believe that hepatectomy and early intervention will maximize patients' benefits.
- bile duct diseases /
- choledochal cyst /
- hepatectomy /
- diagnosis

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参考文献(28)

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