布-加综合征亚型分型的专家共识

中国医师协会腔内血管学专业委员会腔静脉阻塞专家委员会

doi:10.3969/j.issn.1001-5256.2017.07.005

布-加综合征亚型分型的专家共识

DOI: 10.3969/j.issn.1001-5256.2017.07.005

中国医师协会腔内血管学专业委员会腔静脉阻塞专家委员会

基金项目:

江苏省科技支撑计划临床专项项目(BL2012021)；

详细信息

中图分类号: R575
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出版历程
- 收稿日期: 2017-06-07
- 出版日期: 2017-07-20

Expert consensus on the classification of subtype in Budd-Chiari syndrome

Expert committee on Vane Cava Obstruction, Specialized Committee of Endovascology, Chinese Medical Doctor Association

Research funding:

摘要

摘要:
徐州医科大学附属医院介入科于2012-2015年间承担了江苏省科技支撑计划临床专项项目《布-加综合征介入诊疗规范化研究》课题（编号:BL2012021）,经过3年临床研究,结合20余年2150余例的病例总结,2016年1月14日在徐州市召开了布加综合征介入诊疗规范化研究论证会,来自中国医师协会腔内血管学专业委员会腔静脉阻塞专家委员会及国内从事布-加综合征研究的介入放射学、血管外科学、病理学和影像诊断学专家就布-加综合症分型与亚型的划分进行了充分和深入的讨论,与会专家一致达成亚型界定的共识:肝静脉阻塞亚型为肝静脉/副肝静脉膜性阻塞、肝静脉节段性阻塞、肝静脉广泛性阻塞、肝静脉阻塞伴血栓形成;下腔静脉阻塞亚型为下腔静脉膜性带孔阻塞、下腔静脉膜性阻塞、下腔静脉节段性阻塞、下腔静脉阻塞伴血栓形成。混合型亚型为肝静脉和下腔静脉阻塞、肝静脉和下腔静脉阻塞伴血栓形成,共10个亚型。
- 布加综合征 /
- 分型 /
- 亚型 /
- 共识
Abstract:
From 2012 to 2015 the Department of Interventional Radiology of the Affiliated Hospital of Xuzhou Medical University undertook the clinical special research subject” Study on the standardization of interventional diagnosis and treatment of Budd-Chiari syndrome” (No.BL2012021) , a program supported by the Department of Science and Technology of Jiangsu Province.Based on the clinical results of three years research and the scientific summary of the experience from more than 2150 cases accumulated in more than 20 years, the Department of Interventional Radiology of the Affiliated Hospital of Xuzhou Medical University presided over a demonstration meeting about “the standardization of interventional diagnosis and treatment of Budd-Chiari syndrome” on January 14, 2016 in Xuzhou City of Jiangsu Province, China.The scholars from the Expert Committee on Vena Cava Obstruction of Specialized Committee of Endovascology, Chinese Medical Doctor Association, as well as the experts from the related medical fields, including interventional radiology, vascular surgery, pathology and diagnostic imaging, who have been engaged in the study of Budd-Chiari syndrome, attended the meeting, and in the meeting the participants made a full and thorough discussion on the classification and subtypes of Budd-Chiari syndrome.The scholars and experts have unanimously reached a consensus on the subtype definition of Budd-Chiari syndrome:the Budd Chiari syndrome is suggested to be classified into the hepatic vein occlusion subtype, the inferior vena cava occlusion subtype and mixed occlusion subtype, including 10 subtype entities in total.The hepatic vein occlusion subtype includes membranous occlusion of hepatic vein/accessory hepatic vein, segmental occlusion of hepatic vein, extensive occlusion of hepatic vein, and hepatic vein occlusion associated with thrombus formation.The inferior vena cava occlusion subtype includes inferior vena cava membranous occlusion with hole in membrane, inferior vena cava membranous occlusion, segmental occlusion of inferior vena cava, and inferior vena cava occlusion with thrombus formation.The mixed occlusion subtype includes occlusion of hepatic vein and inferior vane cava, and occlusion of hepatic vein and inferior vane cava associated with thrombus formation.
- Budd-Chiari syndrome /
- classfication /
- subtype /
- consensus

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参考文献(34)

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