Primary biliary cholangitis:opportunities and challenges
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摘要: 原发性胆汁性胆管炎是一种累及肝小叶间胆管的自身免疫性肝病,可进展为肝硬化、肝功能衰竭。早期诊断和治疗可显著改善患者预后,提高生活质量。将2017年欧洲肝病学会《原发性胆汁性胆管炎临床实践指南》与实际临床经验相结合,重点评述我国原发性胆汁性胆管炎研究取得的进展和遇到的难点问题。Abstract: Primary biliary cholangitis (PBC) is an autoimmune liver disease mainly involving the interlobular bile ducts and can progress to liver cirrhosis and liver failure.Early diagnosis and management can significantly improve the prognosis of such patients and their quality of life.This article focuses on the achievements of PBC research and related difficult issues in China, with reference to the clinical practice guidelines for PBC by European Association for the Study of the Liver in 2017 and experience in clinical practice.
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Key words:
- cholangitis, biliary /
- diagnosis /
- therapy /
- editorial
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