先天性肝纤维化合并lgG4相关性疾病1例报告

李正鑫; 邢枫; 周扬; 陈高峰; 刘成海

doi:10.3969/j.issn.1001-5256.2018.10.026

先天性肝纤维化合并lgG4相关性疾病1例报告

DOI: 10.3969/j.issn.1001-5256.2018.10.026

1. 上海中医药大学附属曙光医院肝病研究所
2. 上海中医药大学附属曙光医院肝硬化科

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中图分类号: R575.2
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出版历程
- 出版日期: 2018-10-20

A case of congenital hepatic fibrosis with lgG4-related disease

Institute of Liver Diseases, Shuguang Hospital, Shanghai University of Traditional Chinese Medicine

摘要

摘要:
<正>先天性肝纤维化(congenital hepatic fibrosis,CHF)诊断复杂,发病年龄以青少年为主,成人先天性肝纤维化发病较晚,通常以门静脉高压为主要临床表现,出血风险较高。成人CHF合并lg G4升高病例尚未见临床报道。为总结诊断和治疗CHF的经验,现报道如下。1病例资料患者女性,66岁,2014年10月因哮喘服中药数月后出现腹部不适,于外院就诊,发现转氨酶升高,自身抗体阴性,lgG4
- 先天性肝纤维化 /
- 免疫球蛋白G /
- 活组织检查 /
- 病例报告
- congenital hepatic fibrosis /
- immunoglobulin G /
- biopsy /
- case reports

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参考文献(15)

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