以布加综合征为首发表现的阵发性睡眠性血红蛋白尿症1例报告

巫凯敏; 曹珊; 张国艳; 陈国栋; 苏琳; 王智峰; 刘玉兰

doi:10.3969/j.issn.1001-5256.2018.10.028

以布加综合征为首发表现的阵发性睡眠性血红蛋白尿症1例报告

DOI: 10.3969/j.issn.1001-5256.2018.10.028

1. 北京大学人民医院心血管内科
2. 北京大学人民医院消化内科

详细信息

中图分类号: R575;R556.64
计量
- 文章访问数: 2037
- HTML全文浏览量: 5
- PDF下载量: 353
- 被引次数: 0
出版历程
- 出版日期: 2018-10-20

A case of paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome as the first manifestation

Department of Cardiology, Peking University People's Hospital

摘要

摘要:
<正>1病例资料患者女性,24岁,因"腹围增大9个月余,发现肝脏增大7个月余"于本院就诊。患者9个月余前(孕26周)自觉腹围增长迅速,伴有腹壁静脉曲张,无恶心呕吐,无视物模糊,于本院查血常规:WBC 5. 88×10~9/L,Hb 84 g/L,PLT 52×10~9/L,ALT26 U/L,AST 40 U/L,TBil 22. 2μmol/L,DBil 7. 9μmol/L,Alb
- Budd-Chiari综合征 /
- 血红蛋白尿,阵发性 /
- 病例报告
- Budd-Chiari syndrome /
- hemoglobinuria, paroxysmal /
- case reports

HTML全文

参考文献(13)

[1]Red Blood Cell Disease (Anemia) Group, Hematology Society, Chinese Medical Association.Chinese expert consensus on diagnosis and treatment of paroxysmal nocturnal hemoglobinuria[J].Chin J Hematol, 2013, 34 (3) :276-279. (in Chinese) 中华医学会血液学分会红细胞疾病 (贫血) 学组.阵发性睡眠性血红蛋白尿症诊断与治疗中国专家共识[J].中华血液学杂志, 2013, 34 (3) :276-279.

[2]VALLA DC.Primary Budd-Chiari syndrome[J].J Hepatol, 2009, 50 (1) :195-203.

[3]Expert Committee on Vena Cara Obstruction, Specialized Committee of Endovascology, Chinese Medical Doctor Association.Expert consensus on the classification of subtypes in Budd-Chiari syndrome[J].J Intervent Radiol, 2017, 26 (3) :195-201. (in Chinese) 中国医师协会腔内血管学专业委员会腔静脉阻塞专家委员会.布加综合征亚型分型的专家共识[J].介入放射学杂志, 2017, 26 (3) :195-201.

[4]YU H, SUN DX, LIANG ZH, et al.Diagnosis and interventional therapy for Budd-Chiari syndrome secondary to hepatic venous obstruction[J].J Clin Hepatol, 2017, 33 (7) :1340-1341. (in Chinese) 于宏, 孙殿兴, 梁志会, 等.肝静脉阻塞型布加综合征的诊断及介入治疗[J].临床肝胆病杂志, 2017, 33 (7) :1340-1341.

[5]DARWISH MURAD S, PLESSIER A, HERNANDEZ GUERRA M, et al.Etiology, management, and outcome of the Budd-Chiari syndrome[J].Ann Intern Med, 2009, 151 (3) :167-175.

[6]VALLA DC.Budd-Chiari syndrome/hepatic venous outflow tract obstruction[J].Hepatol Int, 2018, 12 (Suppl 1) :168-180.

[7]QI XS, HAN GH, GUO XZ, et al.The aetiology of primary Budd-Chiari syndrome-differences between the West and China[J].Aliment Pharmacol Ther, 2016, 44 (11-12) :1152-1167.

[8]QI XS, HAN GH, GUO XZ, et al.Thrombotic risk factors in Chinese Budd-Chiari syndrome patients:An observational study with a systematic review of the literature[J].Thromb Haemost, 2013, 109 (5) :878-884.

[9]CHENG DL, XU H, LU ZJ, et al.Clinical features and etiology of Budd-Chiari syndrome in Chinese patients:A single-center study[J].J Gastroenterol Hepatol, 2013, 28 (6) :1061-1067.

[10]KESTEVEN P, HANLEY, J, LOUGHNEY A.Pregnance-associated venous thrombosis[J].Phlebology, 2012, 27 (Suppl 2) :s73-s80.

[11]REN WR, LI X, JIA J, et al.Prevalence of Budd-Chiari syndrome during pregnancy or puerperium:A systematic review and meta-analysis[J].Gastroenterol Res Pract, 2015, 2015:839875.

[12]GARCIA-PAGAN JC, HEYDTMANN M, RAFFA S, et al.TIPS for Budd-Chiari syndrome:Long-term results and prognostics factors in124 patients[J].Gastroenterology, 2008, 135 (3) :808-815.

[13]QI XS, HE CY, HAN GH, et al.Prevalence of paroxysmal nocturnal hemoglobinuria in Chinese patients with Budd-Chiari syndrome or portal vein thrombosis[J].J Gastroenterol Hepatol, 2013, 28 (1) :148-152.

施引文献

资源附件(0)

访问统计