VHL syndrome with multiple pancreatic cysts and fourth ventricle hemangioblastoma: A case report
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摘要:
<正>范希佩尔-林道(von Hippel Lindau,VHL)综合征是一组临床上较为罕见的多发性、家族性、累及多系统、多脏器的良恶性肿瘤综合征。可累及到的主要器官有脑、脊髓、视网膜、肾脏、肾上腺、胰腺或者附睾等[1]。德国眼科医生von Hippel在1904年第一个描述了眼球内血管瘤的病例,以及Lindau在1927年描述了小脑及脊髓内血管瘤的病例,后人以两位科学家的名字命名此病[2]。本文总结1例VHL综合征患者资料,希
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Key words:
- pancreatic cyst /
- hemangioblastoma /
- central nervous system neoplasms /
- case reports
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