Guidelines for diagnosing & treating biliary atresia (2018 Edition)
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摘要:
<正>胆道闭锁(biliary atresia,BA)是婴儿期常见的严重肝胆系统疾病之一,以肝内、外胆管进行性炎症和纤维化为特征;如不及时治疗,晚期会出现胆汁性肝硬化、门静脉高压、肝衰竭。目前早期诊断困难,手术治疗效果欠佳,可能与诊断方法、Kasai手术标准化程度及该病知识普及程度有关。制订一个明确、可靠并在临床上切实可行的指南是当下亟需解决的问题。本指南涵盖近年来相关研究,将所有证据基于GRADE系
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Key words:
- biliary atresia /
- child /
- practice guidelines as topic
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