左半肝切除术治疗Schnelldorfer C型多囊肝1例报告

曾齐; 沙地克·阿帕尔; 吴警; 努尔扎提江·安维尔; 李涛; 吐尔洪江·吐逊

doi:10.3969/j.issn.1001-5256.2020.08.032

左半肝切除术治疗Schnelldorfer C型多囊肝1例报告

DOI: 10.3969/j.issn.1001-5256.2020.08.032

新疆医科大学第一附属医院消化血管外科中心肝(移植)·腔镜外科

基金项目:

新疆维吾尔自治区科技厅重点实验室开放课题项目(2018D04002)；新疆维吾尔自治区天山青年计划博士科技人才培养项目(2017Q094)；

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出版历程
- 出版日期: 2020-08-20

Left hemihepatectomy for Schnelldorfer type C polycystic liver disease: A case report

Department of Liver Transplantation & Laparoscopic Surgery, Digestive & Vascular Surgery Center, The First Affiliated Hospital of Xinjiang Medical University

Research funding:

摘要

摘要:
<正>多囊肝（polycystic liver disease,PLD）是一类罕见的基因病,既可作为常染色体显性PLD单独存在,也可伴随常显或常隐多囊肾[1]。PLD的主要特点是胆管上皮细胞的过度生长,表现为肝实质多个弥散分布的囊性病变,常与成人多囊肾伴发。该病早期常无典型的症状及体征,肝功能正常,但中晚期随着肝体积的增大可出现腹胀、腹痛及腹部包块,影响患者的正常生活[2]。目前的治疗方式主要分为内科药物治疗和外科手术
- 多囊肝 /
- 多囊肾疾病 /
- 肝切除术
- polycystic liver disease /
- polycystic kidney diseases /
- hepatectomy

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参考文献(13)

[1] BAE KT,ZHU F,CHAPMAN AB,et al. Magnetic resonance imaging evaluation of hepatic cysts in early autosomal-dominant polycystic kidney disease:The Consortium for Radiologic Imaging Studies of Polycystic Kidney Disease cohort[J]. Clin J Am Soc Nephrol,2006,1(1):64-69.

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[5] GIGOT JF,JADOUL P,QUE F,et al. Adult polycystic liver disease:Is fenestration the most adequate operation for long-term management?[J]. Ann Surg,1997,225(3):286-294.

[6] SCHNELLDORFER T,TORRES VE,ZAKARIA S,et al. Polycystic liver disease:A critical appraisal of hepatic resection,cyst fenestration,and liver transplantation[J]. Ann Surg,2009,250(1):112-118.

[7] DAN AA,YOUNOSSI ZM. Quality of life and liver transplantation in patients with polycystic liver disease[J]. Liver Transpl,2006,12(8):1184-1185.

[8] BERNTS L,DRENTH J,TJWA E. Management of portal hypertension and ascites in polycystic liver disease[J]. Liver Int,2019,39(11):2024-2033.

[9] MACUTKIEWICZ C,PLASTOW R,CHRISPIJN M,et al. Complications arising in simple and polycystic liver cysts[J].World J Hepatol,2012,4(12):406-411.

[10] XU XL,GAO CC,WANG ZX,et al. Advances in the diagnosis and treatment of cystic space-occupying lesions in the liver[J]. J Clin Hepatol,2019,35(5):1118-1122.(in Chinese)许晓磊，高灿灿，王志鑫，等．肝囊性占位性病变的诊断与治疗[J]．临床肝胆病杂志，2019,35(5):1118-1122.

[11] AUSSILHOU B,DOKMAK S,DONDERO F,et al. Treatment of polycystic liver disease. Update on the management[J]. J Visc Surg,2018,155(6):471-481.

[12] van AERTS R,van de LAARSCHOT L,BANALES JM,et al.Clinical management of polycystic liver disease[J]. J Hepatol,2018,68(4):827-837.

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