原发性胆汁性胆管炎合并自身免疫性溶血性贫血1例报告

吴蓉; 冷爱民

doi:10.3969/j.issn.1001-5256.2020.12.030

原发性胆汁性胆管炎合并自身免疫性溶血性贫血1例报告

DOI: 10.3969/j.issn.1001-5256.2020.12.030

吴蓉,
冷爱民

中南大学湘雅医院消化内科

详细信息

中图分类号: R556.6;R575.7
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出版历程
- 出版日期: 2020-12-20

Primary biliary cirrhosis with autoimmune hemolytic anemia: A case report

WU Rong,
LING AiMin

Department of Gastroenterology,Xiangya Hospital,Central South University

摘要

摘要:
<正>原发性胆汁性胆管炎（PBC）是一种慢性肝内胆汁淤积性疾病,其病理特点为进行性、非化脓性、破坏性肝内小胆管炎,最终可发展至肝硬化[1]。80%以上的PBC患者常合并至少1种自身免疫性疾病,其中干燥综合征是较为常见的[2]。而PBC合并自身免疫性溶血性贫血（autoimmune hemolytic anemia,AIHA）的病例报告尚不多,现将中南大学湘雅医院收治的1例PBC合并AIHA病例报告如下,并总结国内外近10年报道的诊断为PBC伴AIHA的8例患者临床资料,对以上9例患者的临床特征、实验室检查结果及治疗转归等方面进行分析,以提高临床医生对本病的认识,旨在为临床诊断与治疗提供更科学的理论依据。
- 肝硬化,胆汁性 /
- 胆汁淤积 /
- 贫血,溶血性,自身免疫性
- liver cirrhosis,biliary /
- cholestasis /
- anemia,hemolytic,autoimmune

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参考文献(27)

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