《IgG4相关性疾病诊治中国专家共识》解读

周佳鑫; 张文

doi:10.3969/j.issn.1001-5256.2021.09.012

《IgG4相关性疾病诊治中国专家共识》解读

DOI: 10.3969/j.issn.1001-5256.2021.09.012

周佳鑫,
张文^,

中国医学科学院北京协和医院风湿免疫科，国家皮肤和免疫性疾病临床研究中心，教育部重点实验室，疑难重症和罕见病国家重点实验室，北京 100730

基金项目:

首都卫生发展科研专项基金 (2020-2-4017);

中国医学科学院中央级公益性科研院所基本科研业务费专项资金资助 (2019XK320038);

国家自然基金面上项目 (82071839)

利益冲突声明：所有作者均声明不存在利益冲突。

作者贡献声明：周佳鑫参与起草及修改文章关键内容；张文负责确定文章的思路及论文框架设计。

详细信息

通信作者:
张文，zhangwen91@sina.com

中图分类号: R593.2
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- 被引次数: 0
出版历程
- 收稿日期: 2021-08-16
- 录用日期: 2021-08-16
- 出版日期: 2021-09-20

Interpretation of Chinese expert consensus on the diagnosis and treatment of IgG4-related diseases

Jiaxin ZHOU,
Wen ZHANG^,

National Clinical Research Center for Dermatologic and Immunologic Diseases, Key Laboratory of Ministry of Education, National Key Laboratory of Difficult Severe Diseases and Rare Diseases, Department of Rheumatology, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences, Beijing 100730, China

Research funding:

The Capital's Funds for Health Improvement and Research (2020-2-4017);

the Non-profit Central Research Institute Fund of Chinese Academy of Medical Sciences (2019XK320038);

the National Natural Science Foundation of China (82071839)

摘要

摘要: IgG4相关性疾病(IgG4-RD)是一种以受累脏器慢性炎症伴纤维化为特征表现的免疫介导的疾病。近年来，我国学者对该病的认识逐渐深入，积累了较多的诊治经验，并于2020年在中国罕见病联盟和中华医学会风湿病学分会的平台上，由专家组制定了首个《IgG4相关性疾病诊治的中国专家共识》。该共识较全面概括了IgG4相关性疾病的诊治原则，为临床医生对该病的诊治提供了较好的依据。现就该指南的内容进行解读。
- 免疫球蛋白G /
- 诊断 /
- 治疗学 /
- 共识
Abstract: IgG4-related disease (IgG4-RD) is an immune-mediated disease characterized by chronic inflammation and fibrosis of affected organs. With a deeper understanding of this disease among Chinese scholars and the rich experience in diagnosis and treatment in recent years, an expert group was organized by China Alliance for Rare Diseases and Chinese Rheumatology Association in 2020 and developed the first Chinese expert consensus on the diagnosis and treatment of IgG4-related diseases. This consensus comprehensively summarizes the principles of the diagnosis and treatment of IgG4-RD and thus provides a basis for its diagnosis and treatment by clinicians.
- Immunoglobulin G /
- Diagnosis /
- Therapeutics /
- Consensus

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参考文献(42)

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