先天性肝外门体分流的研究进展

王莹; 徐声润; 余荻; 杨晋辉; 常江

doi:10.3969/j.issn.1001-5256.2023.02.032

先天性肝外门体分流的研究进展

DOI: 10.3969/j.issn.1001-5256.2023.02.032

昆明医科大学第二附属医院消化内科，昆明 650101

利益冲突声明： 所有作者均声明不存在利益冲突。

作者贡献声明： 王莹负责查阅文献，撰写文章；徐声润、余荻提供修改意见并参与修改；杨晋辉指导选题及写作思路；常江提供修改意见并最终定稿。

详细信息

通信作者:
常江，cjcjchangjiang@sina.com (ORCID: 0000-0002-8678-3979)

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出版历程
- 收稿日期: 2022-06-29
- 录用日期: 2022-07-30
- 出版日期: 2023-02-20

Research advances in congenital extrahepatic portosystemic shunt

Department of Gastroenterology, The Second Affiliated Hospital of Kunming Medical University, Kunming 650101, China

More Information

Corresponding author: CHANG Jiang, cjcjchangjiang@sina.com (ORCID: 0000-0002-8678-3979)

摘要

摘要: 先天性肝外门体分流(CEPS)也称Abernethy畸形，表现为先天性门静脉与下腔静脉之间存在异常吻合。该病在临床上极为罕见，加之其症状表现多样，易漏诊误诊。本文就CEPS的发生机制、分型特点、临床表现、诊断及治疗等研究进展作一综述，以期提高对CEPS的认识，并为其诊治流程的进一步规范提供参考。
- 先天性肝外门体分流 /
- Abernethy畸形 /
- 诊断 /
- 治疗学
Abstract: Congenital extrahepatic portosystemic shunt (CEPS) is also called Abernethy malformation, with the manifestation of congenital abnormal anastomosis between the portal vein and the inferior vena cava. CEPS is extremely rare in clinical practice and has diverse clinical symptoms, which often leads to missed diagnosis and misdiagnosis. This article reviews the pathogenesis, classification, clinical manifestation, diagnosis, and treatment of CEPS, so as to improve the awareness of this disease and provide a reference for further standardization of its diagnosis and treatment process in the future.
- Congenital Extrahepatic Portosystemic Shunt /
- Abernethy Malformation /
- Diagnosis /
- Therapeutics

HTML全文

图 1 CEPS分型

注：SV，脾静脉；SMV，肠系膜上静脉；IVC，下腔静脉；PV，门静脉。

Figure 1. Classification of CEPS

下载: 全尺寸图片幻灯片

图 2 CEPS诊治流程

Figure 2. Diagnosis and treatment process of CEPS

下载: 全尺寸图片幻灯片

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