IgG4-related autoimmune pancreatitis with Mikulicz's disease: a report of one case
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摘要: <正>IgG4相关疾病是近年来被认识的一种可以累及多个器官并以血清中IgG4水平升高、受累器官大量IgG4阳性浆细胞浸润为主要特征的疾病[1]。本病在日本及韩国屡有发生,在我国目前罕见报道。本文就本院收治的1例IgG4相关的自身免疫性胰腺炎重叠米库利奇病患者作如下报道。1临床资料男性患者,63岁,吉林白山市人。因腹胀1 a,双侧腮腺及颌下腺肿大伴唾液分泌障碍6个月于2012年11月5日入院。
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Key words:
- pancreatitis /
- autoimmune diseases /
- sjogren's syndrome /
- case reports
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[1]MASAKI Y, KUROSE N, UMEHARA H.IgG4-related disease:a novel lymphoproliferative disorder discovered and established in Japan in the 21stcentury[J].J Clin Exp Hematop, 2011, 51 (1) :13-20. [2]SUGUMAR A, KLPPEL G, CHARI ST.Autoimmune pancreatitis:pathologic subtypes and their implications for its diagnosis[J].Am J Gastroenterol, 2009, 104 (9) :2308-2310. [3]KAMISAWA T, RYU JK, KIM MH, et al.Recent advances in the diagnosis and management of autoimmune pancreatitis:similarities and differences in Japan and Korea[J].Gut Liver, 2013, 7 (4) :394-400. [4]HIMI T, TAKANO K, YAMAMOTO M.A novel concept of Mikulicz's disease as IgG4-related disease[J].Auris Nasus Larynx, 2012, 39 (1) :9-17.
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