Research progress in causes of congenital biliary atresia
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摘要:
先天性胆道闭锁是一种发病机制尚未完全清楚的多病因、多表型的新生儿罕见疾病,当前对其病因学研究的热点主要集中于病毒感染、免疫失调以及发育异常等方面。归纳了目前先天性胆道闭锁主流的病因假说及各假说之间的联系,认为这些研究进展为病因探索和新的防治手段提供了宝贵的线索和依据。
Abstract:Congenital biliary atresia is considered a neonatal rare disease with multiple causes and phenotypes,whose pathogenesis remains unclear. At present,the etiological study of congenital biliary atresia mainly focuses on viral infection,immune disorder,and dysplasia.This paper summarizes the main etiological hypotheses about congenital biliary atresia nowadays and the connections between them. The research progress provides valuable clues and evidence for the etiology and control of this disease.
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Key words:
- biliary atresia /
- etiology /
- infant,newbern /
- review
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