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摘要: <正>噬血细胞综合征(hemophagocytic syndrome,HPS)按病因可分为原发性和继发性,原发性HPS于1952年由Farquhar等首次报道,继发性HPS于1975年由Chandra首次报道。但其诊断及治疗目前尚缺乏相关的临床经验。本文主要介绍本科收治的1例以黄疸为突出表现的妊娠合并HPS的病例资料,旨在为临床鉴别妊娠期肝功能受损的患者提供参考。
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关键词:
- 淋巴组织细胞增多症,嗜血细胞性 /
- 妊娠 /
- 病例报告
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Key words:
- lymphohistiocytosis,hemophagocytic /
- pregnancy /
- case reports
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[1]RAMOS-CASALS M,BRITO-ZERN P,LPEZ-GUILLERMO A,et al.Adult haemophagocytic syndrome[J].Lancet,2014,9927(383):1503-1516. [2]HU Q,ZHANG XL.Diagnostic guidelines for hemophagocytic syndrome(2004)[J].J Appl Clin Pediatr,2008,23(3):235-236.(in Chinese)胡群,张小玲,噬血细胞综合征诊断指南(2004)[J].实用儿科临床杂志,2008,23(3):235-236. [3]HENTER JI,HORNE A,ARICO M,et al.HLH-2004,Diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis[J].Pediatr Blood Cancer,2007,48(2):124-131. [4]GUO X,LI Q,ZHOU CY.Retrospective analysis of 41 childhood hemophagocytic syndrome[J].Chin J Hepatol,2007,28(7):449-453.(in Chinese)郭霞,李强,周晨燕.儿童噬血细胞综合征41例临床分析[J].中华血液学杂志,2007,28(7):449-453. [5]CHEN BH,LI HY,XU XM,et al.Pregnancy complicated by hemophagocytic syndrome:a clinical analysis of 3 cases[J].Chin J Obstetr Gynecol,2012,47(4):301-302.(in Chinese)陈宝花,李会云,徐先明,等.妊娠合并噬血细胞综合征三例临床分析[J].中华妇产科杂志,2012,47(4):301-302. [6]WANG XL,WANG Z.Advance in acquired hemophagocytic syndrome[J].Chin J Med,2010,90(14):1004-1006.(in Chinese)王晓琳,王昭.获得性噬血细胞综合征研究进展[J].中华医学杂志,2010,90(14):1004-1006. [7]WANG H,GAO WJ,LIU AS,et al.Retrospective and predictive analysis of 54 children with hemophagocytic syndrome[J].J China Pediatric Blood Cancer,2013,18(1):31-34.(in Chinese)王华,高文瑾,刘安生,等,儿童噬血细胞综合征54例临床级预后因素分析[J].中国小儿血液与肿瘤杂志,2013,18(1):31-34.
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