Pathological features of hepatic vascular diseases and key points in differential diagnosis
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摘要: 肝血管病是累及肝脏循环系统的一组异质性疾病。尽管肝血管病的发病率普遍较低,但却是发生门静脉高压症的一个重要原因。该类患者的发病年龄通常较小,误诊、误治可明显降低患者的预期寿命。熟练掌握肝血管病的临床表现、影像学及病理形态学特点,对于明确诊断及制订合理的治疗策略至关重要。重点介绍了常见肝血管病的病理特点及鉴别诊断要点。Abstract: Hepatic vascular diseases are a group of heterogeneous diseases which affect blood circulation in the liver. Although hepatic vascular diseases have a low incidence rate, they remain an important cause of portal hypertension. Patients often develop these diseases at a younger age, and misdiagnosis and/or mistreatment may greatly reduce their life expectancy. A good understanding of clinical manifestations, imaging features, and pathological features of hepatic vascular diseases is of vital importance in clarifying diagnosis and developing reasonable treatment strategies. This article introduces the pathological features of common hepatic vascular diseases and key points in differential diagnosis.
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Key words:
- liver diseases /
- vascular diseases /
- pathology /
- diagnosis, differential
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