原发性胆汁性胆管炎合并特殊原因所致贫血1例报告

张晓雪; 冯丽娜; 陈庆灵; 蒉乙文; 杨倩倩; 温晓玉; 金清龙

doi:10.3969/j.issn.1001-5256.2020.04.038

原发性胆汁性胆管炎合并特殊原因所致贫血1例报告

DOI: 10.3969/j.issn.1001-5256.2020.04.038

1. 吉林大学第一医院肝胆胰内科
2. 中国科学院大学宁波华美医院消化内科

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中图分类号: R556;R575.7
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出版历程
- 出版日期: 2020-04-20

Anemia caused by primary biliary cholangitis and special reasons: A case report

Department of Hepatology,The First Hospital of Jilin University

摘要

摘要: <正>原发性胆汁性胆管炎（PBC）是一种慢性肝内胆汁淤积性疾病。其病理特点为进行性、非化脓性、破坏性肝内小胆管炎,最终可发展至肝硬化。目前,熊去氧胆酸是唯一经随机对照临床试验证实治疗本病安全有效的药物[1]。贫血是肝硬化常见表现之一,除非合并上消化道出血或叶酸缺乏,很少引起严重贫血,如果不能找到引起贫血的原因,单纯对症治疗易导致贫血反复发作,因此准确判断贫血病因是治疗的关键。现报道1例PBC合并特殊原因所致反复贫血的病例,以提高对此病的认识。
- 肝硬化,胆汁性 /
- 贫血 /
- 贫血,溶血性,自身免疫性
- liver cirrhosis,biliary /
- anemia /
- anemia,hemolytic,autoimmune

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参考文献(16)

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