Autoimmune pancreatitis(AIP) is a special type of chronic pancreatitis that originates from an autoimmune-mediated mechanism.AIP has unique radiological,serological,and histopathological features,often accompanied by peripancreatic lesions.AIP may be easily confused with pancreatic cancer and cholangiocarcinoma.It is necessary to diagnose AIP while integrating a variety of clinical indicators.Steroid therapy should be performed for patients diagnosed with AIP,and surgical treatment can be selected if necessary.