[1]BEUERS U,GERSHWIN ME,GISH RG,et al.Changing nomenclature for PBC:from‘cirrhosis’to‘cholangitis’[J].Gut,2015,64(11):1671-1672.
|
[2]SHAPIRO JM,SMITH H,SCHAFFNER F.Serum bilirubin:a prognostic factor in primary biliary cirrhosis[J].Gut,1979,20(2):137-140.
|
[3]ROLL J,BOYER JL,BARRY D,et al.The prognostic importance of clinical and histologic features in asymptomatic and symptomatic primary biliary cirrhosis[J].N Engl J Med,1983,308(1):1-7.
|
[4]CHRISTENSEN E,NEUBERGER J,CROWE J,et al.Beneficial effect of azathioprine and prediction of prognosis in primary biliary cirrhosis.Final results of an international trial[J].Gastroenterology,1985,89(5):1084-1091.
|
[5]DICKSON ER,GRAMBSCH PM,FLEMING TR,et al.Prognosis in primary biliary cirrhosis:model for decision making[J].Hepatology 1989,10(1):1-7.
|
[6]PRINCE M,CHETWYND A,NEWMAN W,et al.Survival and symptom progression in a geographically based cohort of patients with primary biliary cirrhosis:follow-up for up to 28 years[J].Gastroenterology,2002,123(4):1044-1051.
|
[7]HEATHCOTE EJ.Management of primary biliary cirrhosis.The American Association for the Study of Liver Diseases practice guidelines[J].Hepatology,2000,31(4):1005-1013.
|
[8]ANGULO P,LINDOR KD,THERNEAU TM,et al.Utilization of the Mayo risk score in patients with primary biliary cirrhosis receiving ursodeoxycholic acid[J].Liver,1999,19(2):115-121.
|
[9]CORPECHOT C,ABENAVOLI L,RABAHI N,et al.Biochemical response to ursodeoxycholic acid and long-term prognosis in primary biliary cirrhosis[J].Hepatology,2008,48(3):871-877.
|
[10]CHAN AW,CHAN RC,WONG GL,et al.New simple prognostic score for primary biliary cirrhosis:albumin-bilirubin score[J].JGastroenterol Hepatol,2015,30(9):1391-1396.
|
[11]JOHNSON PJ,BERHANE S,KAGEBAYASHI C,et al.Assessment of liver function in patients with hepatocellular carcinoma:a new evidence-based approach-the ALBI grade[J].J Clin Oncol,2015,33(6):550-558.
|
[12]KUMAGI T,GUINDI M,FISCHER SE,et al.Baseline ductopenia and treatment response predict long-term histological progression in primary biliary cirrhosis[J].Am J Gastroenterol,2010,105(10):2186-2194.
|
[13]CORPECHOT C,CHAZOUILLRES O,POUPON R.Early primary biliary cirrhosis:biochemical response to treatment and prediction of long-term outcome[J].J Hepatol,2011,55(6):1361-1367.
|
[14]AZEMOTO N,ABE M,MURATA Y,et al.Early biochemical response to ursodeoxycholic acid predicts symptom development in patients with asymptomatic primary biliary cirrhosis[J].J Gastroenterol,2009,44(6):630-634.
|
[15]LAMMERS WJ,van BUUREN HR,HIRSCHFIELD GM,et al.Levels of alkaline phosphatase and bilirubin are surrogate end points of outcomes of patients with primary biliary cirrhosis:an international follow-up study[J].Gastroenterology,2014,147(6):1338-1349.
|
[16]PARS A,CABALLERA L,RODS J.Excellent long-term survival in patients with primary biliary cirrhosis and biochemical response to ursodeoxycholic acid[J].Gastroenterology,2006,130(3):715-720.
|
[17]KUIPER EM,HANSEN BE,de VRIES RA,et al.Improved prognosis of patients with primary biliary cirrhosis that have a biochemical response to ursodeoxycholic acid[J].Gastroenterology,2009,136(4):1281-1287.
|
[18]FLOREANI A,CAZZAGON N,MARTINES D,et al.Performance and utility of transient elastography and noninvasive markers of liver fibrosis in primary biliary cirrhosis[J].Dig Liver Dis,2011,43(11):887-892.
|
[19]CORPECHOT C,CARRAT F,POUJOL-ROBERT A,et al.Noninvasive elastography-based assessment of liver fibrosis progression and prognosis in primary biliary cirrhosis[J].Hepatology,2012,56(1):198-208.
|
[20]DUAN WJ,ZHANG FK,OU XJ,et al.The clinical profiles of primary biliary cirrhosis with a suboptimal biochemical response to ursodeoxycholic acid[J].Chin J Hepatol,2011,19(2):118-120.(in Chinese)段维佳,张福奎,欧晓娟,等.原发性胆汁性肝硬化患者对熊去氧胆酸应答欠佳的影响因素分析[J].中华肝脏病杂志,2011,19(2):118-120.
|
[21]CARBONE M,SHARP SJ,FLACK S,et al.The UK-PBC risk scores:derivation and validation of a scoring system for long-term prediction of end-stage liver disease in primary biliary cholangitis[J].Hepatology,2016,63(3):930-950.
|
[22]LAMMERSWJ,HIRSCHFIELD GM,CORPECHOT C,et al.Development and validation of a scoring system to predict outcomes of patients with primary biliary cirrhosis receiving ursodeoxycholic acid therapy[J].Gastroenterology,2015,149(7):1804-1812.
|
[23]Chinese Society of Hepatology,Chinese Medical Association;Chinese Society of Gastroenterology,Chinese Medical Association;Chinese Society of Infectious Diseases,Chinese Medical Association.Consensus on the diagnosis and management of primary biliary cirrhosis(cholangitis)(2015)[J].J Clin Hepatol,2015,31(12):1980-1988.(in Chinese)中华医学会肝病学分会,中华医学会消化病学分会,中华医学会感染病学分会.原发性胆汁性肝硬化(又名原发性胆汁性胆管炎)诊断和治疗共识(2015)[J].临床肝胆病杂志,2015,31(12):1980-1988.
|
[24]LEUSCHNER M,MAIER KP,SCHLICHTING J,et al.Oral budesonide and ursodeoxycholic acid for treatment of primary biliary cirrhosis:results of a prospective double-blind trial[J].Gastroenterology,1999,117(4):918-925.
|
[25]ANGULO P,JORGENSEN RA,KEACH JC,et al.Oral budesonide in the treatment of patients with primary biliary cirrhosis with a suboptimal response to ursodeoxycholic acid[J].Hepatology,2000,31(2):318-323.
|
[26]RAUTIAINEN H,KRKKINEN P,KARVONEN AL,et al.Budesonide combined with UDCA to improve liver histology in primary biliary cirrhosis:a three-year randomized trial[J].Hepatology,2005,41(4):747-752.
|
[27]RABAHI N,CHRTIEN Y,GAOUAR F,et al.Triple therapy with ursodeoxycholic acid,budesonide and mycophenolate mofetil in patients with features of severe primary biliary cirrhosis not responding to ursodeoxycholic acid alone[J].Gastroenterol Clin Biol,2010,34(4-5):283-287.
|
[28]RAUTIAINEN H,KARVONEN AL,KARKKAINEN P,et al.6year follow up of liver histology after budesonide to UDCA combination therapy in PBC compared with UDCA monoterapy[J].J Hepatol,2011,54(Suppl):s517.
|
[29]RAUTIAINEN H,FRKKILM,NEUVONEN M,et al.Pharmacokinetics and bone effects of budesonide in primary biliary cirrhosis[J].Aliment Pharmacol Ther,2006,24(11-12):1545-1552.
|
[30]NEVENS F,ANDREONE P,MAZZELLA G,et al.The first primary biliary cirrhosis(PBC)phase 3 trial in two decades---an international study of the FXR agonist obeticholic acid[J].J Hepatol,2014,60:s525.
|
[31]HIRSCHFIELD GM,MASON A,LUKETIC V,et al.Efficacy of obeticholic acid in patients with primary biliary cirrhosis and inadequate response to ursodeoxycholic acid[J].Gastroenterology,2015,148(4):751-761.
|
[32]IWASAKI S,OHIRA H,NISHIGUCHI S,et al.The efficacy of ursodeoxycholic acid and bezafibrate combination therapy for primary biliary cirrhosis:a prospective,multicenter study[J].Hepatol Res,2008,38(6):557-564.
|
[33]KANDA T,YOKOSUKA O,IMAZEKI F,et al.Bezafibrate treatment:a new medical approach for PBC patients?[J].J Gastroenterol,2003,38(6):573-578.
|
[34]ITAKURA J,IZUMI N,NISHIMURA Y,et al.Prospective randomized crossover trial of combination therapy with bezafibrate and UDCA for primary biliary cirrhosis[J].Hepatol Res,2004,29(4):216-222.
|
[35]LEVY C,PETER JA,NELSON DR,et al.Pilot study:fenofibrate for patients with primary biliary cirrhosis and an incomplete response to ursodeoxycholic acid[J].Aliment Pharmacol Ther,2011,33(2):235-242.
|
[36]LENS S,LEOZ M,NAZAL L,et al.Bezafibrate normalizes alkaline phosphatase in primary biliary cirrhosis patients with incomplete response to ursodeoxycholic acid[J].Liver Int,2014,34(2):197-203.
|
[37]CORPECHOT C.Primary biliary cirrhosis beyond ursodeoxycholic acid[J].Semin Liver Dis,2016,36(1):15-26.
|
[38]SUN LM,WANG YP,LIU YM,et al.Differential characteristics ofA-MA-M2 autoantibody in primary biliary cirrhosis and non-PBC patients[J].Chin J Hepatol,2015,23(5):343-349.(in Chinese)孙丽梅,王一鹏,刘燕敏,等.抗线粒体抗体M2亚型在非原发性胆汁性肝硬化患者中的特点[J].中华肝脏病杂志,2015,23(5):343-349.
|
[39]de LEMOS AS,FOUREAU DM,JACOBS C,et al.Drug-induced liver injury with autoimmune features[J].Semin Liver Dis,2014,34(2):194-204.
|
[40]LIU YM,LIAO HY,YAN HP,et al.A clinical study of bilirubin rise in short-term in patients with primary biliary cirrhosis[J].Chin J Hepatol,2012,20(8):632-633.(in Chinese)刘燕敏,廖慧钰,闫惠平,等.原发性胆汁性肝硬化患者胆红素短期内上升临床分析[J].中华肝脏病杂志,2012,20(8):632-633.
|
[41]European Association for the Study of the Liver.EASL clinical practice guidelines:management of cholestatic liver diseases[J].JHepatol,2009,51(2):237-267.
|